Prune Belly Syndrome in Sagamu: Report of Three Cases with Typical and Atypical Features

Abstract

Summary: Prune belly is a rare congenital anomaly. that is commonly seen in males. We report two male cases and a phenotypic female with absent abdominal wall musculature that were seen within one year at the Olabisi Onabanjo University Teaching Hospital, Sagamu. These cases are reported to create a better awareness of this disorder in this environment. This, to our knowledge, is the first report of prune belly syndrome in our centre.  Maternal age, the precise aetiology is uncertain. However, sex influenced autosomal mode of inheritance has been suggested. 8, 9 While there have been reports of this syndrome from Ibadan, the exact incidence in Nigeria is unknown. It is probably rare but it is also likely that some cases are missed in clinical practice due to poor awareness and constraints in investigation, In view of this, we are reporting three cases of prune belly syndrome seen in Sagamu, within a period of one year.