Pentalogy of Cantrell - A Case Report from Nigeria

Authors

  • Mukhtar-Yola M ( ) Department of Surgery
  • Mohammad AM Department of Surgery
  • Faroul ZL Department of Paediatrics
  • Alhassan SU Department of Surgery
  • Adeleke SI Department of Paediatrics
  • Aji AA Department of Surgery
  • Asani MO

Abstract

Abstract: FB was delivered at home to a para three low income mothe r, a t t e rm a f t e r an unsupervised pregnancy. At birth
she was noticed to have an anterior chest wall defect with a protruding p u l s a t i n g ma s s . F u r t h e r examination revealed a defect from the suprasternal notch to the xiphoid process (bifid sternum) with the heart exposed and pulsating (ectopia cordis).  The pericardium was absent and the great vessels were exposed. There was an epigastric omphalocoele and a ventral diaphragmatic defect. The diagnosis of Pentallogy of Cantrell was made. The challenges involved in the evaluation and management of this case in a Nigerian setting are discussed.

Keywords: Pentallogy, Cantrell, Nigeria.

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Published

2024-07-02

Issue

Vol. 39 No. 1 (2012): Nigerian Journal of Paediatrics

Section

CASE REPORTS

License

This is an open-access journal, and articles are distributed under the terms of the Creative Commons Attribution 4.0 License, which allows others to remix, transform, and build upon the work even, commercially, as long as appropriate credit is given to the author, and the new creations are licensed under identical terms

How to Cite

Pentalogy of Cantrell - A Case Report from Nigeria. (2024). NIGERIAN JOURNAL OF PAEDIATRICS, 39(1), 31-34. https://www.njpaediatrics.com/index.php/njp/article/view/479