Frontonasal encephalocele with bilateral congenital microblepharon: A case report

Authors

  • Ochoga MO Department of Paediatrics
  • Idoko A Department of Paediatrics
  • Abah RO Department of Paediatrics
  • Obande JO Department of Surgery

Abstract

Abstract: A six-day old term neonate was born with a frontonasal ulcerated discharging mass with purulent fluid but no cerebrospinal fluid. The left eye socket was empty and there was bilateral microblepharon. Computerized tomography scan showed irregular shaped soft tissue mass, the same density as the brain tissue, continuous with the frontal lobe and associated defect of frontal bone/nasium. The mass displaced the left globe inferiorly but there was a demarcation between the globe and the mass. Ventricular systems were grossly dilated and distorted (lateral and 3rd ventricles). However, the 4th ventricle was normal. We present a patient with an unusual constellation of clinical and radiologic findings that have not been, hitherto described.

Key words: Frontonasal, encephalocele, neural tube defect, midline defects, microblepharon

Author Biographies

  • Ochoga MO, Department of Paediatrics



    Benue State University/Benue State
    University Teaching Hospital,
    Makurdi

  • Idoko A, Department of Paediatrics


    Benue State University/Benue State
    University Teaching Hospital,
    Makurdi

  • Abah RO, Department of Paediatrics


    Benue State University/Benue State
    University Teaching Hospital,
    Makurdi

     

  • Obande JO, Department of Surgery

    University of Abuja, Teaching Hospital,
    Gwagwalada-Abuja

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Published

2024-07-02

How to Cite

Frontonasal encephalocele with bilateral congenital microblepharon: A case report. (2024). NIGERIAN JOURNAL OF PAEDIATRICS, 44(4), 193-195. https://www.njpaediatrics.com/index.php/njp/article/view/152