Idiopathic basal ganglia calcifica- tion (Fahr’s disease) in a 9 - year - old Nigerian child

Authors

  • Okike O Clifford Department of Paediatrics
  • Ajaegbu C Obinna Department of Paediatrics
  • Origbo Lazerus Department of Paediatrics
  • Muoneke V Uzoamaka Department of Paediatrics

Abstract

Abstract: Fahr’s disease is a rare neurodegenerative disorder characterized by deposition of calcium on the walls of blood vessels of the Basal ganglia and Dentate nuclei of the Cerebellum. Patient can present with diverse array of symptoms including but not limited to seizure, extrapyramidal symptoms and mental retardation. We report a case of a 9 year old female child with history of recurrent seizure. Brain CT showed symmetrical calcification in the basal ganglia.

Keywords: Fahr’s syndrome, intracranial calcification, seizure

Author Biographies

  • Okike O Clifford, Department of Paediatrics
    Federal Medical Center Asaba, Delta State
  • Ajaegbu C Obinna, Department of Paediatrics
      Federal Medical Center Asaba, Delta State
  • Origbo Lazerus, Department of Paediatrics
    Federal Medical Center Asaba, Delta State
  • Muoneke V Uzoamaka, Department of Paediatrics
      College of Medical Sciences, University of Nigeria, Enugu Campus, Enugu State

Published

2021-03-01

Issue

Vol. 48 No. 1 (2021): Nigerian Journal of Paediatrics

Section

CASE REPORTS

License

This is an open-access journal, and articles are distributed under the terms of the Creative Commons Attribution 4.0 License, which allows others to remix, transform, and build upon the work even, commercially, as long as appropriate credit is given to the author, and the new creations are licensed under identical terms

How to Cite

Idiopathic basal ganglia calcifica- tion (Fahr’s disease) in a 9 - year - old Nigerian child. (2021). NIGERIAN JOURNAL OF PAEDIATRICS, 48(1), 46 – 49. https://www.njpaediatrics.com/index.php/njp/article/view/25